Table 3 Functional cardiac MRI information from a subset of 20 individuals with Proteus syndrome who underwent cardiac MRI.
Parameter (units) | Individuals with fat (n = 9) | Individuals without fat (n = 11) | P-value | ||
|---|---|---|---|---|---|
Range | Mean ± SD | Range | Mean ± SD | ||
LVEF (%) | 53–69 | 60 ± 5 | 55–67 | 61 ± 4 | 0.56 |
LVEDV (ml) | 64–245 | 132 ± 50 | 75–228 | 140 ± 42 | 0.72 |
LVESV (ml) | 20–111 | 55 ± 26 | 25–103 | 55 ± 20 | 0.99 |
LVSV (ml) | 44–134 | 77 ± 25 | 46–125 | 85 ± 23 | 0.50 |
CO (ml/min) | 4–9 | 6 ± 1.5 | 4–8 | 6 ± 1 | 0.77 |
LVEDVI (ml/m2) | 60–123 | 83 ± 19 | 63–121 | 84 ± 17 | 0.90 |
LVESVI (ml/m2) | 21–49 | 33.5 ± 8 | 22–55 | 33 ± 10 | 0.93 |
LVSVI (ml/m2) | 34–80 | 50 ± 13 | 38–66 | 51 ± 8 | 0.81 |
CI (ml/min/m2) | 2–8.5 | 4 ± 2 | 3–5 | 4 ± 1 | 0.82 |
AS (mm) | 4–13 | 7 ± 3 | 4–9 | 6 ± 1 | 0.30 |
PL (mm) | 4–10 | 6 ± 1.5 | 3–7 | 6 ± 1 | 0.94 |