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Table 3 Functional cardiac MRI information from a subset of 20 individuals with Proteus syndrome who underwent cardiac MRI.

From: Cardiothoracic imaging findings of Proteus syndrome

Parameter (units)

Individuals with fat (n = 9)

Individuals without fat (n = 11)

P-value

Range

Mean ± SD

Range

Mean ± SD

LVEF (%)

53–69

60 ± 5

55–67

61 ± 4

0.56

LVEDV (ml)

64–245

132 ± 50

75–228

140 ± 42

0.72

LVESV (ml)

20–111

55 ± 26

25–103

55 ± 20

0.99

LVSV (ml)

44–134

77 ± 25

46–125

85 ± 23

0.50

CO (ml/min)

4–9

6 ± 1.5

4–8

6 ± 1

0.77

LVEDVI (ml/m2)

60–123

83 ± 19

63–121

84 ± 17

0.90

LVESVI (ml/m2)

21–49

33.5 ± 8

22–55

33 ± 10

0.93

LVSVI (ml/m2)

34–80

50 ± 13

38–66

51 ± 8

0.81

CI (ml/min/m2)

2–8.5

4 ± 2

3–5

4 ± 1

0.82

AS (mm)

4–13

7 ± 3

4–9

6 ± 1

0.30

PL (mm)

4–10

6 ± 1.5

3–7

6 ± 1

0.94

  1. LVEF = left ventricular ejection fraction, LVEDV = left ventricular end-diastolic volume, LVESV = left ventricular end-systolic volume, LVSV = left ventricular stroke volume, CO = cardiac output, LVEDVI = left ventricular end-diastolic volume index, LVESVI = left ventricular end-systolic volume index, LVSVI = left ventricular stroke volume index, CI = cardiac index, AS = anteroseptal wall thickness, PL = posterolateral wall thickness.